A three year old girl was brought by her parents with generalised tonic clonic seizures. The patient had been started on anti-epileptic medication after similar episodes at one year of age. However, the seizures were frequent and unresponsive to the medication.
Axial and coronal T2W and coronal FLAIR images of the brain show hemiatrophy of the left cerebral hemisphere - predominantly involving the left temporal lobe with widening of the sulcal spaces, decreased volume of the cortex and the white matter. There is mild ipsilateral ventriculomegaly. There is atrophy of the left hippocampus.
PET images show hypometabolism in the left cerebral hemisphere.
Named for the neurosurgeon Theodore Rasmussen (1910–2002), who succeeded Wilder Penfield as head of the Montreal Neurological Institute and first described the condition in 1958